Multiple cylindroma of the scalp
- Authors: Vertieva E.Y.1, Teplyakova K.S.1
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Affiliations:
- I.M. Sechenov First Moscow State Medical University (Sechenov University)
- Issue: Vol 24, No 4 (2021)
- Pages: 329-334
- Section: DERMATO-ONCOLOGY
- URL: https://rjsvd.com/1560-9588/article/view/80212
- DOI: https://doi.org/10.17816/dv80212
- ID: 80212
Cite item
Abstract
Cylindroma is a rare benign tumor derived from the skin appendages, its typical localization is head and neck. The histogenesis of the disease is unknown, cylindromas are thought to develop from the epithelial ducts of the eccrine or apocrine glands, or represent a neoplastic proliferation of epithelial stem cells.
The clinical presentation of the disease includes single or multiple smooth nodules and nodes of a pale pink color. Branching vessels are often visualized on their surface.
There are two types of this tumor: sporadic genetically not determined сylindroma and inherited in an autosomal dominant manner multiple сylindroma.
Multiple cylindroma may cause a lesion on the scalp that looks like a turban, due to the fusion and an increasing size of the nodules. Therefore, cylindroma are sometimes called a turban tumor.
The treatment of multiple cylindroma is a serious interdisciplinary problem due to the large area of the lesion, abundant blood supply to the scalp and the tendency of the disease to recur. The treatment methods described in the literature include traditional surgical excision, electrocoagulation, laser, Mohs micrographic surgery.
In this article we present a rare clinical case of a young male diagnosed with multiple cylindroma.
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About the authors
Ekaterina Yu. Vertieva
I.M. Sechenov First Moscow State Medical University (Sechenov University)
Author for correspondence.
Email: ivertieva@gmail.com
ORCID iD: 0000-0002-1088-2911
SPIN-code: 3712-8453
MD, Cand. Sci. (Med.)
Russian Federation, MoscowKseniya S. Teplyakova
I.M. Sechenov First Moscow State Medical University (Sechenov University)
Email: hvpvea@gmail.com
ORCID iD: 0000-0002-0428-5627
SPIN-code: 5983-9344
Graduate Student
Russian Federation, MoscowReferences
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