Erythrosis pigmentosa peribuccalis Brocq

Pigmented peribuccal erythrosis of Brocq is a rare disease, with less than 50 cases reported in the literature, affecting mainly women. The dermatosis manifests itself as small follicular pigmented and slightly hyperkeratotic papules that are grouped centrofacially to form plaques with clear contours around the mouth and nose, sometimes with lesions in the forehead. The color intensity may change during the day, due to the presence of a vascular component. The dermatosis does not cause subjective symptoms and the main complaints of patients are reduced to aesthetic discomfort due to the sharp transition from orange-brown coloring around the mouth and nose to the normal color of the cheeks. The etiology of this condition is currently unknown, the features of the dermatoscopic picture have not been described, and standardized and effective methods of therapy have not been developed.

This article describes the clinical manifestations and dermatoscopic picture of this rare dermatosis in a 23-year-old girl with a disease duration of 6 years and ineffectiveness of previous treatment, who had pronounced and persistent positive dynamics against the background of treatment of concomitant cystic ovarian formations, the use of external agents with a keratolytic effect and strict photoprotection.